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dc.contributor.author
Semprino, Marcos
dc.contributor.author
Galicchio, Santiago
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Espeche, Alberto
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Cersosimo, Ricardo
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Chacon, Santiago
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Gamboni, Beatriz
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Adi, Javier
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Fasulo, Lorena
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Fortini, Sebastian
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Cachia, Pedro
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Gallo, Adolfo
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Caraballo, Roberto Horacio
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dc.date.available
2023-02-06T17:37:17Z
dc.date.issued
2022-03
dc.identifier.citation
Semprino, Marcos; Galicchio, Santiago; Espeche, Alberto; Cersosimo, Ricardo; Chacon, Santiago; et al.; Panayiotopoulos syndrome: Unusual clinical manifestations; Academic Press Inc Elsevier Science; Epilepsy & Behavior (print); 128; 3-2022; 1-7
dc.identifier.issn
1525-5050
dc.identifier.uri
http://hdl.handle.net/11336/187044
dc.description.abstract
Purpose: We retrospectively analyzed the electroclinical features, treatment, and outcome of patients with Panayiotopoulos syndrome (PS) who presented with unusual clinical manifestations. Method: A retrospective, descriptive, multicenter study was conducted evaluating 44 patients with PS who had seizures with an unusual semiology. Data from patients with PS seen at eight Argentine centers between April 2000 and April 2019 were collected. Results: Twelve patients (29.2%) had ictal syncope or syncope-like epileptic seizures. Three children (7.3%) had recurrent episodes of vomiting. Four patients (9.7%) presented with urinary incontinence associated with autonomic signs and consciousness impairment. One child had hiccups with autonomic manifestations followed by eye deviation. One boy had episodes of laughter with autonomic symptoms followed by loss of consciousness. Six patients (14.6%) had hyperthermia without acute febrile illness with autonomic symptoms as the first manifestation. Six others (14.6%) had focal motor seizures characterized by eye and head deviation in four and eyelid blinking in two. Four patients (9.7%) had ictal headache as the initial manifestation followed by nausea and vomiting. Two children (4.8%) had their first seizure while asleep associated with cardiorespiratory arrest. Two children (4.8%) had oral automatisms, such as sucking and chewing. In two children (4.8%) coughing was the initial manifestation followed by emetic symptoms. One patient (2.3%) had vertigo with a sensation of fear, with eye deviation and unresponsiveness. One child started with continuous spikes and waves during slow sleep, behavior disturbances, and emetic symptoms. Conclusion: In this study, evidence of the existence of unusual clinical cases of PS with typical EEG patterns was found. Outcome was excellent.
dc.format
application/pdf
dc.language.iso
eng
dc.publisher
Academic Press Inc Elsevier Science
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dc.rights
info:eu-repo/semantics/restrictedAccess
dc.rights.uri
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.subject
AUTONOMIC SEIZURES
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CHILDHOOD
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EPILEPSY
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FOCAL
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PANAYIOTOPOULOS SYNDROME
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SELF-LIMITED
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Neurología Clínica
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dc.subject.classification
Medicina Clínica
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dc.subject.classification
CIENCIAS MÉDICAS Y DE LA SALUD
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dc.title
Panayiotopoulos syndrome: Unusual clinical manifestations
dc.type
info:eu-repo/semantics/article
dc.type
info:ar-repo/semantics/artículo
dc.type
info:eu-repo/semantics/publishedVersion
dc.date.updated
2023-02-06T10:15:57Z
dc.journal.volume
128
dc.journal.pagination
1-7
dc.journal.pais
Estados Unidos
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dc.description.fil
Fil: Semprino, Marcos. Clínica San Lucas; Argentina
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Fil: Galicchio, Santiago. Hospital de Niños Victor J Vilela de Rosario; Argentina
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Fil: Espeche, Alberto. Gobierno de la Provincia de Salta. Hospital Publico Materno Infantil.; Argentina
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Fil: Cersosimo, Ricardo. Centro Integral de Neurociencias; Argentina
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Fil: Chacon, Santiago. Centro de Neurología Infantil; Argentina
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Fil: Gamboni, Beatriz. Gobierno de la Provincia de Mendoza. Hospital Pediátrico Humberto Notti; Argentina
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Fil: Adi, Javier. Gobierno de la Provincia de Mendoza. Hospital Pediátrico Humberto Notti; Argentina
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Fil: Fasulo, Lorena. Clínica San Lucas; Argentina
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Fil: Fortini, Sebastian. Provincia de Tucuman. Ministerio de Salud. Sistema Provincial de Salud. Hospital del Ni?o Jesus; Argentina
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Fil: Cachia, Pedro. Hospital de Niños Victor J Vilela de Rosario; Argentina
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Fil: Gallo, Adolfo. Gobierno de la Ciudad de Buenos Aires. Hospital de Pediatría "Juan P. Garrahan"; Argentina
dc.description.fil
Fil: Caraballo, Roberto Horacio. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Gobierno de la Ciudad de Buenos Aires. Hospital de Pediatría "Juan P. Garrahan"; Argentina
dc.journal.title
Epilepsy & Behavior (print)
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dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/url/https://www.sciencedirect.com/science/article/pii/S1525505022000014
dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/doi/http://dx.doi.org/10.1016/j.yebeh.2022.108552
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