Artículo
Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review
Fecha de publicación:
03/2021
Editorial:
Springer
Revista:
Current Urology Reports (print)
ISSN:
1527-2737
Idioma:
Inglés
Tipo de recurso:
Artículo publicado
Clasificación temática:
Resumen
Purpose of Review: To update epidemiological, diagnostic, and therapeutic information on primary synovial sarcoma of the kidney. Recent Findings: A total of 96 studies were analyzed; age at presentation was 38.6±14.2 years, predominant location of tumor was right kidney; frequent reported symptoms at diagnosis were hematuria and pain. For definitive diagnosis, cytogenetic technique was used. Detected oncogene was available in 37.8% cases with fusion of SS18-SSX in most patients. Surgery is treatment of choice, with adjuvant chemotherapy; most frequently ifosfamide-based associated with doxorubicin or epirubicin. Overall median survival was 34 months. Mortality was 29% of the cases which reported death and the recurrence rate was 39.8%. Risk of death was increased in patients with metastases at diagnosis Summary: Primary RSS occurs more often in young men. RSS often presents with symptoms and in an advanced stage. Surgical treatment is the most commonly used and chemotherapy for advanced or recurrent treatment.
Palabras clave:
KIDNEY
,
PRIMARY RENAL SYNOVIAL SARCOMA
,
RENAL SARCOMA
,
RENAL TUMOR
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Licencia
Identificadores
Colecciones
Articulos(CIESP)
Articulos de CENTRO DE INVESTIGACIONES EN EPIDEMIOLOGIA Y SALUD PUBLICA
Articulos de CENTRO DE INVESTIGACIONES EN EPIDEMIOLOGIA Y SALUD PUBLICA
Citación
Blas, Leandro; Roberti, Javier Eugenio; Primary Renal Synovial Sarcoma and Clinical and Pathological Findings: a Systematic Review; Springer; Current Urology Reports (print); 22; 4; 3-2021; 1-13
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