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dc.contributor.author
Gresele, Paolo
dc.contributor.author
Falcinelli, Emanuela
dc.contributor.author
Bury, Loredana
dc.contributor.author
Pecci, Alessandro
dc.contributor.author
Alessi, Marie Christine
dc.contributor.author
Borhany, Munira
dc.contributor.author
Heller, Paula Graciela
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dc.contributor.author
Santoro, Cristina
dc.contributor.author
Cid, Ana Rosa
dc.contributor.author
Orsini, Sara
dc.contributor.author
Fontana, Pierre
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De Candia, Erica
dc.contributor.author
Podda, Gianmarco
dc.contributor.author
Kannan, Meganathan
dc.contributor.author
Jurk, Kerstin
dc.contributor.author
Castaman, Giancarlo
dc.contributor.author
Falaise, Céline
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Guglielmini, Giuseppe
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Noris, Patrizia
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Zaninetti, Carlo
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Fiore, Mathieu
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Tosseto, Alberto
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Zuñiga, Pamela
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Miyazaki, K.
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Dupuis, Arnaud
dc.contributor.author
Hayward, Catherine
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Casonatto, Alessandra
dc.contributor.author
Grandone, Elvira
dc.contributor.author
Mazzuconi Maria Gabriella
dc.contributor.author
James, Paula
dc.contributor.author
Fabris, Fabrizio
dc.contributor.author
Henskens, Yvonne
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Napolitano, Mariasanta
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Curnow, Jennifer
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Gkalea, Vasiliki
dc.contributor.author
Fedor, Marian
dc.contributor.author
Lambert, Michele P.
dc.contributor.author
Zieger, Barbara
dc.contributor.author
Barcella, Luca
dc.contributor.author
Cosmi, Benilde
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Giordano, Paola
dc.contributor.author
Porri, Claudia
dc.contributor.author
Melazzini, Federica
dc.contributor.author
Abid, Madiha
dc.contributor.author
Glembotsky, Ana Claudia
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dc.contributor.author
Ferrara, Gracia
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Russo, Alessandra
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Deckmyn, Hans
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Frelinger, Andrew L.
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Harrison, Paul
dc.contributor.author
Mezzano, Diego
dc.contributor.author
Mumford, Andrew D.
dc.contributor.author
Lordkipanidzé, Marie
dc.date.available
2022-09-01T14:05:03Z
dc.date.issued
2021-05
dc.identifier.citation
Gresele, Paolo; Falcinelli, Emanuela; Bury, Loredana; Pecci, Alessandro; Alessi, Marie Christine; et al.; The ISTH bleeding assessment tool as predictor of bleeding events in inherited platelet disorders: Communication from the ISTH SSC Subcommittee on Platelet Physiology; Wiley Blackwell Publishing, Inc; Journal of Thrombosis and Haemostasis; 19; 5; 5-2021; 1364-1371
dc.identifier.issn
1538-7933
dc.identifier.uri
http://hdl.handle.net/11336/167162
dc.description.abstract
Background: The ISTH Bleeding Assessment Tool (ISTH-BAT) has been validated for clinical screening of suspected von Willebrand disease (VWD) and for bleeding prediction. Recently it has been validated for subjects with inherited platelet disorders (IPD) (BAT-VAL study). Objectives: To determine whether the ISTH-BAT bleeding score (BS) predicts subsequent bleeding events requiring treatment in IPD patients. Methods: Patients with IPD, type 1 VWD (VWD-1) and age- and sex-matched healthy controls enrolled in the BAT-VAL study were prospectively followed-up for 2 years and bleeding episodes requiring treatment were recorded. Results: Of the 1098 subjects initially enrolled, 955 were followed-up and 124 suffered hemorrhages during follow-up, 60% of whom had inherited platelet function disorders (IPFD). Total number of events was significantly higher in IPFD (n = 235) than VWD-1 (n = 52) or inherited thrombocytopenia (IT; n = 20). Events requiring transfusions were 66% in IPFD, 5.7% in VWD-1, and 3% in IT. Baseline BS was significantly higher in IPFD patients with a bleeding event at follow-up than in those without (p <.01) and the percentage of subjects suffering a bleeding event increased proportionally to baseline BS quartile. A significant association between the BS and the chance of suffering severe bleeding was found in the overall, IPFD, and VWD-1 populations. Similar results were obtained for the pediatric population. Conclusions: Inherited platelet function disorder patients with high BS at enrollment are more likely to suffer from bleeding events requiring treatment at follow-up. Moreover, the higher the baseline BS quartile the greater the incidence of subsequent events, suggesting that independently from diagnosis a high BS is associated with a greater risk of subsequent hemorrhage.
dc.format
application/pdf
dc.language.iso
eng
dc.publisher
Wiley Blackwell Publishing, Inc
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dc.rights
info:eu-repo/semantics/restrictedAccess
dc.rights.uri
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.subject
BLEEDING PREDICTION
dc.subject
BLEEDING SCORE
dc.subject
INHERITED PLATELET DISORDERS
dc.subject
MILD-MODERATE BLEEDING DISORDERS
dc.subject
VON WILLEBRAND DISEASE
dc.subject.classification
Hematología
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dc.subject.classification
Medicina Clínica
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dc.subject.classification
CIENCIAS MÉDICAS Y DE LA SALUD
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dc.title
The ISTH bleeding assessment tool as predictor of bleeding events in inherited platelet disorders: Communication from the ISTH SSC Subcommittee on Platelet Physiology
dc.type
info:eu-repo/semantics/article
dc.type
info:ar-repo/semantics/artículo
dc.type
info:eu-repo/semantics/publishedVersion
dc.date.updated
2022-08-25T12:40:44Z
dc.journal.volume
19
dc.journal.number
5
dc.journal.pagination
1364-1371
dc.journal.pais
Reino Unido
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dc.journal.ciudad
Londres
dc.description.fil
Fil: Gresele, Paolo. Università di Perugia; Italia
dc.description.fil
Fil: Falcinelli, Emanuela. Università di Perugia; Italia
dc.description.fil
Fil: Bury, Loredana. Università di Perugia; Italia
dc.description.fil
Fil: Pecci, Alessandro. Universita degli Studi di Pavia; Italia
dc.description.fil
Fil: Alessi, Marie Christine. Center For Cardiovascular And Nutrition Research; Francia
dc.description.fil
Fil: Borhany, Munira. National Institute Of Blood Diseases And Bone Marrow Transplantation; Pakistán
dc.description.fil
Fil: Heller, Paula Graciela. Consejo Nacional de Investigaciones Científicas y Técnicas. Oficina de Coordinación Administrativa Houssay. Instituto de Investigaciones Médicas. Universidad de Buenos Aires. Facultad de Medicina. Instituto de Investigaciones Médicas; Argentina
dc.description.fil
Fil: Santoro, Cristina. Azienda Policlinico Umberto I; Italia
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Fil: Cid, Ana Rosa. Hospital Universitario y Politecnico La Fe; España
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Fil: Orsini, Sara. Università di Perugia; Italia
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Fil: Fontana, Pierre. Hôpitaux Universitaires de Genève; Suiza
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Fil: De Candia, Erica. Fondazione Policlinico Agostino Gemelli; Italia. Università Cattolica del Sacro Cuore; Italia
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Fil: Podda, Gianmarco. Università degli Studi di Milano; Italia
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Fil: Kannan, Meganathan. Central University Of Tamil Nadu; India
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Fil: Jurk, Kerstin. Johannes Gutenberg Universitat Mainz; Alemania
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Fil: Castaman, Giancarlo. Careggi University Hospital; Italia
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Fil: Falaise, Céline. Center For Cardiovascular And Nutrition Research; Francia
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Fil: Guglielmini, Giuseppe. Università di Perugia; Italia
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Fil: Noris, Patrizia. Universita degli Studi di Pavia; Italia
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Fil: Zaninetti, Carlo. Universita degli Studi di Pavia; Italia
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Fil: Fiore, Mathieu. Universita degli Studi di Pavia; Italia
dc.description.fil
Fil: Tosseto, Alberto. San Bortolo Hospital; Italia
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Fil: Zuñiga, Pamela. Pontificia Universidad Católica de Chile; Chile
dc.description.fil
Fil: Miyazaki, K.. Kitasato University School of Medicine; Japón
dc.description.fil
Fil: Dupuis, Arnaud. Université de Strasbourg; Francia
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Fil: Hayward, Catherine. Mc Master University; Canadá
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Fil: Casonatto, Alessandra. Università di Padova; Italia
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Fil: Grandone, Elvira. Ospedale Casa Sollievo della Sofferenza; Italia
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Fil: Mazzuconi Maria Gabriella. Università degli Studi di Roma "La Sapienza"; Italia
dc.description.fil
Fil: James, Paula. Queens University; Canadá
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Fil: Fabris, Fabrizio. Università di Padova; Italia
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Fil: Henskens, Yvonne. University Medical Centre; Países Bajos
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Fil: Napolitano, Mariasanta. Università degli Studi di Palermo; Italia
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Fil: Curnow, Jennifer. Westmead Hospital; Australia
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Fil: Gkalea, Vasiliki. Tenon University Hospital; Italia
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Fil: Fedor, Marian. Svet Zdravia; Eslovaquia
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Fil: Lambert, Michele P.. Children's Hospital of Philadelphia; Estados Unidos
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Fil: Zieger, Barbara. University Medical Center Freiburg; Alemania
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Fil: Barcella, Luca. ASST Papa Giovanni XXIII; Italia
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Fil: Cosmi, Benilde. Universidad de Bologna; Italia
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Fil: Giordano, Paola. Università degli Studi di Bari; Italia
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Fil: Porri, Claudia. Hospital Italiano; Argentina
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Fil: Melazzini, Federica. Universita degli Studi di Pavia; Italia
dc.description.fil
Fil: Abid, Madiha. National Institute of Blood Disease & Bone Marrow Transplantation; Pakistán
dc.description.fil
Fil: Glembotsky, Ana Claudia. Consejo Nacional de Investigaciones Científicas y Técnicas. Oficina de Coordinación Administrativa Houssay. Instituto de Investigaciones Médicas. Universidad de Buenos Aires. Facultad de Medicina. Instituto de Investigaciones Médicas; Argentina
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Fil: Ferrara, Gracia. Azienda Ospedaliera Universitaria Policlinico Umberto I; Italia
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Fil: Russo, Alessandra. Johannes Gutenberg Universitat Mainz; Alemania
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Fil: Deckmyn, Hans. KU Leuven Campus Kulak Kortrijk; Bélgica
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Fil: Frelinger, Andrew L.. Harvard Medical School; Estados Unidos
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Fil: Harrison, Paul. University of Birmingham Medical School; Reino Unido
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Fil: Mezzano, Diego. Pontificia Universidad Católica de Chile; Chile
dc.description.fil
Fil: Mumford, Andrew D.. University of Bristol; Reino Unido
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Fil: Lordkipanidzé, Marie. Montreal Heart Institute; Canadá
dc.journal.title
Journal of Thrombosis and Haemostasis
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dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/url/https://onlinelibrary.wiley.com/doi/10.1111/jth.15263
dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/doi/http://dx.doi.org/10.1111/jth.15263
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