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dc.contributor.author
Bailez, Maria Marcela
dc.contributor.author
Costanzo, Mariana
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dc.contributor.author
Guercio, Gabriela Viviana
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dc.date.available
2022-04-05T14:39:59Z
dc.date.issued
2021-08
dc.identifier.citation
Bailez, Maria Marcela; Costanzo, Mariana; Guercio, Gabriela Viviana; Role of minimally invasive surgery (MIS) in different sexual development (DSD); Elsevier Science Inc.; Seminars In Pediatric Surgery; 30; 4; 8-2021; 1-12
dc.identifier.issn
1055-8586
dc.identifier.uri
http://hdl.handle.net/11336/154377
dc.description.abstract
Differences/disorders of sex development (DSD) are a heterogeneous group of congenital conditions in which the development of chromosomal, gonadal, or anatomical sex is atypical. Patients usually present during the newborn period but occasionally some cases remain unrecognized until later in infancy or even adolescence. Genital appearance, psychosocial support, sociocultural background, gender identity development, and genetic and biochemical analysis in addition to ethical and legal implications need to be considered when deciding on the appropriate treatment strategy. Surgeons are important members of the multidisciplinary expert teams involved in the initial approach and long-term follow-up. Surgical care of DSD patients is one of the main challenges. Recommendations regarding the opportunity and timing of surgical procedures are still under discussion. Surgical procedures are aimed to reduce urologic problems, prevent the risk of gonadal germ-cell cancer, and facilitate sexual function and reproduction. Providing its excellent visualization, access to pelvic structures and less postoperative adhesion MIS has been an important tool in the diagnosis and treatment of DSD. The role of MIS will be summarized in: 1) Gonadal biopsy / gonadectomy 2) Treatment of urogenital sinus/vaginoplasty 3) Vaginal Replacement 4) Resection / treatment of Mullerian structures
dc.format
application/pdf
dc.language.iso
eng
dc.publisher
Elsevier Science Inc.
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dc.rights
info:eu-repo/semantics/restrictedAccess
dc.rights.uri
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.subject
45XX DSD
dc.subject
46XYDSD
dc.subject
GERM CELL TUMORS IN DSD
dc.subject
MIS GONADAL BIOPSIES
dc.subject
MIS VAGINAL REPLACEMENT
dc.subject
OVOTESTES
dc.subject
PMDS
dc.subject
STREAK GONAD
dc.subject
UROGENITAL SINUS
dc.subject.classification
Cirugía
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dc.subject.classification
Medicina Clínica
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dc.subject.classification
CIENCIAS MÉDICAS Y DE LA SALUD
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dc.title
Role of minimally invasive surgery (MIS) in different sexual development (DSD)
dc.type
info:eu-repo/semantics/article
dc.type
info:ar-repo/semantics/artículo
dc.type
info:eu-repo/semantics/publishedVersion
dc.date.updated
2022-03-14T21:05:07Z
dc.journal.volume
30
dc.journal.number
4
dc.journal.pagination
1-12
dc.journal.pais
Países Bajos
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dc.journal.ciudad
Amsterdam
dc.description.fil
Fil: Bailez, Maria Marcela. Hospital de Pediatra Garrahan; Argentina
dc.description.fil
Fil: Costanzo, Mariana. Hospital de Pediatra Garrahan; Argentina
dc.description.fil
Fil: Guercio, Gabriela Viviana. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Hospital de Pediatra Garrahan; Argentina
dc.journal.title
Seminars In Pediatric Surgery
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dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/doi/http://dx.doi.org/10.1016/j.sempedsurg.2021.151078
dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/url/https://www.sciencedirect.com/science/article/pii/S1055858621000664
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