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dc.contributor.author
Nembhard, Wendy N.
dc.contributor.author
Bergman, Jorieke E. H.
dc.contributor.author
Politis, Maria D.
dc.contributor.author
Arteaga Vázquez, Jazmín
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Bermejo Sánchez, Eva
dc.contributor.author
Canfield, Mark A.
dc.contributor.author
Cragan, Janet
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Dastgiri, Saeed
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de Walle, Hermien E K
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Feldkamp, Marcia L
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Nance, Amy
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Gatt, Miriam
dc.contributor.author
Groisman, Boris
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Hurtado Villa, Paula
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Kallén, Kärin
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Landau, Danielle
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Lelong, Nathalie
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López Camelo, Jorge Santiago
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Martinez, Laura
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Morgan, Margery
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Pierini, Anna
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Rissmann, Anke
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Sípek, Antonin
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Szabova, Elena
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Tagliabue, Giovanna
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Wertelecki, Wladimir
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Zarante, Ignacio
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Bakker, Marian K.
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Kancherla, Vijaya
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Mastroiacovo, Pierpaolo
dc.date.available
2021-11-08T13:14:31Z
dc.date.issued
2020-12
dc.identifier.citation
Nembhard, Wendy N.; Bergman, Jorieke E. H.; Politis, Maria D.; Arteaga Vázquez, Jazmín; Bermejo Sánchez, Eva; et al.; A multi-country study of prevalence and early childhood mortality among children with omphalocele; John Wiley & Sons Inc; Birth Defects Research; 112; 20; 12-2020; 1787-1801
dc.identifier.issn
2472-1727
dc.identifier.uri
http://hdl.handle.net/11336/146223
dc.description.abstract
Background: Omphalocele is the second most common abdominal birth defect and often occurs with other structural and genetic defects. The objective of this study was to determine omphalocele prevalence, time trends, and mortality during early childhood, by geographical region, and the presence of associated anomalies. Methods: We conducted a retrospective study with 23 birth defect surveillance systems in 18 countries who are members of the International Clearinghouse for Birth Defects Surveillance and Research that submitted data on cases ascertained from 2000 through 2012, approximately 16 million pregnancies were surveyed that resulted in live births, stillbirths, or elective terminations of pregnancy for fetal anomalies (ETOPFA) and cases with omphalocele were included. Overall prevalence and mortality rates for specific ages were calculated (day of birth, neonatal, infant, and early childhood). We used Kaplan–Meier estimates with 95% confidence intervals (CI) to calculate cumulative mortality and joinpoint regression for time trend analyses. Results: The prevalence of omphalocele was 2.6 per 10,000 births (95% CI: 2.5, 2.7) and showed no temporal change from 2000–2012 (average annual percent change = −0.19%, p =.52). The overall mortality rate was 32.1% (95% CI: 30.2, 34.0). Most deaths occurred during the neonatal period and among children with multiple anomalies or syndromic omphalocele. Prevalence and mortality varied by registry type (e.g., hospital- vs. population-based) and inclusion or exclusion of ETOPFA. Conclusions: The prevalence of omphalocele showed no temporal change from 2000–2012. Approximately one-third of children with omphalocele did not survive early childhood with most deaths occurring in the neonatal period.
dc.format
application/pdf
dc.language.iso
eng
dc.publisher
John Wiley & Sons Inc
dc.rights
info:eu-repo/semantics/restrictedAccess
dc.rights.uri
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.subject
MORTALITY
dc.subject
OMPHALOCELE
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PREVALENCE
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REGISTRY
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SURVEILLANCE
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Epidemiología
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Ciencias de la Salud
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CIENCIAS MÉDICAS Y DE LA SALUD
dc.title
A multi-country study of prevalence and early childhood mortality among children with omphalocele
dc.type
info:eu-repo/semantics/article
dc.type
info:ar-repo/semantics/artículo
dc.type
info:eu-repo/semantics/publishedVersion
dc.date.updated
2021-09-07T14:56:47Z
dc.journal.volume
112
dc.journal.number
20
dc.journal.pagination
1787-1801
dc.journal.pais
Estados Unidos
dc.description.fil
Fil: Nembhard, Wendy N.. University of Arkansas for Medical Sciences; Estados Unidos
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Fil: Bergman, Jorieke E. H.. University Medical Center; Países Bajos
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Fil: Politis, Maria D.. University of Arkansas for Medical Sciences; Estados Unidos
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Fil: Arteaga Vázquez, Jazmín. Instituto Nacional de Ciencias Médicas y Nutrición; México
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Fil: Bermejo Sánchez, Eva. Instituto de Salud Carlos Iii (isciii); España
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Fil: Canfield, Mark A.. No especifíca;
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Fil: Cragan, Janet. No especifíca;
dc.description.fil
Fil: Dastgiri, Saeed. No especifíca;
dc.description.fil
Fil: de Walle, Hermien E K. University of Groningen; Países Bajos
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Fil: Feldkamp, Marcia L. State University of Utah; Estados Unidos
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Fil: Nance, Amy. No especifíca;
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Fil: Gatt, Miriam. No especifíca;
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Fil: Groisman, Boris. Ministerio de Salud de la Nación; Argentina
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Fil: Hurtado Villa, Paula. Pontificia Universidad Javeriana; Colombia
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Fil: Kallén, Kärin. National Board Of Health And Welfare; Suecia
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Fil: Landau, Danielle. Soroka Medical Center; Israel
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Fil: Lelong, Nathalie. Paris Descartes University; Argentina
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Fil: López Camelo, Jorge Santiago. Consejo Nacional de Investigaciones Científicas y Técnicas. Oficina de Coordinación Administrativa Parque Centenario. CEMIC-CONICET. Centro de Educaciones Médicas e Investigaciones Clínicas "Norberto Quirno". CEMIC-CONICET; Argentina
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Fil: Martinez, Laura. Universidad Autónoma de Nuevo León; México
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Fil: Morgan, Margery. Singleton Hospital; Reino Unido
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Fil: Pierini, Anna. Tuscany Registry of Congenital Defects, Pisa, Italy; Argentina
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Fil: Rissmann, Anke. No especifíca;
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Fil: Sípek, Antonin. Thomayer Hospital; República Checa
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Fil: Szabova, Elena. Slovak Medical University; Eslovaquia
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Fil: Tagliabue, Giovanna. Istituto Nazionale Tumori; Italia
dc.description.fil
Fil: Wertelecki, Wladimir. No especifíca;
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Fil: Zarante, Ignacio. Pontificia Universidad Javeriana; Colombia
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Fil: Bakker, Marian K.. University of Groningen; Países Bajos
dc.description.fil
Fil: Kancherla, Vijaya. University Of Emory. Rollins School Of Public Health; Estados Unidos
dc.description.fil
Fil: Mastroiacovo, Pierpaolo. International Center On Birth Defects; Italia
dc.journal.title
Birth Defects Research
dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/doi/http://dx.doi.org/10.1002/bdr2.1822
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