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dc.contributor.author
Moulin, L.
dc.contributor.author
Pedraza, N.
dc.contributor.author
Padin, J.
dc.contributor.author
Niveyro, S.
dc.contributor.author
Tuhay, G.
dc.contributor.author
Rumbo, C.
dc.contributor.author
Barros Schelotto, Pablo
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dc.contributor.author
Crivelli, A.
dc.contributor.author
Solar Muñiz, H.
dc.contributor.author
Ramisch, D.
dc.contributor.author
Gondolesi, Gabriel Eduardo
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dc.date.available
2018-04-27T19:37:45Z
dc.date.issued
2016-03
dc.identifier.citation
Moulin, L.; Pedraza, N.; Padin, J.; Niveyro, S.; Tuhay, G.; et al.; Case Report: Spleen-preserving Multivisceral Transplant for Peutz–Jeghers Syndrome; Elsevier Science Inc; Transplantation Proceedings; 48; 2; 3-2016; 546-548
dc.identifier.issn
0041-1345
dc.identifier.uri
http://hdl.handle.net/11336/43725
dc.description.abstract
CASE REPORT:A 24-year-old man diagnosed with Peutz-Jeghers syndrome as a child underwent multiple surgeries owing to intussusception. Pretransplant workup showed >150 polyps along the gastrointestinal (GI) tract, some of them with high-grade dysplasia. Despite having intestinal sufficiency, a modified multivisceral transplantation was offered.PROCEDURE:An 18-year-old donor was procured using University of Wisconsin solution. The recipient´s surgery started with a midline incision. Mobilization of the right colon and the root of the mesentery was done to isolate the superior mesenteric artery. The same maneuver was done with the left and sigmoid colon. The common bile duct was then isolated and transected at the cystic duct level. The abdominal portion of the esophagus and the proximal stomach were isolated and divided at the gastroesophageal junction. After that, the pancreas was mobilized, preserving the spleen with the splenic vessels. The distal GI tract was transacted at the level of the proximal rectum. For engraftment, an arterial conduit was placed in the infrarenal aorta and anastomosed to the graft´s aortic patch. End-to-side portal reconstruction was made at the level of the portal vein, allowing performing a duct-to-duct biliary reconstruction over a 5-Fr T-tube. A hand-sewn gastrogastric anastomosis and piloroplasty were performed; the distal anastomosis was done with circular staplers. A gastrojejunostomy and a loop ileostomy were the final steps of the procedure.RESULTS:The patient stayed in intensive care for 2 days and enteral feeds were started on day 7. Currently, 23 months after transplant he is alive with an excellent quality of life
dc.format
application/pdf
dc.language.iso
eng
dc.publisher
Elsevier Science Inc
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dc.rights
info:eu-repo/semantics/openAccess
dc.rights.uri
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.subject
Peutz-Jeghers Syndrome
dc.subject
Multivisceral Transplantation
dc.subject.classification
Medicina Critica y de Emergencia
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dc.subject.classification
Medicina Clínica
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dc.subject.classification
CIENCIAS MÉDICAS Y DE LA SALUD
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dc.title
Case Report: Spleen-preserving Multivisceral Transplant for Peutz–Jeghers Syndrome
dc.type
info:eu-repo/semantics/article
dc.type
info:ar-repo/semantics/artículo
dc.type
info:eu-repo/semantics/publishedVersion
dc.date.updated
2018-04-27T13:59:16Z
dc.journal.volume
48
dc.journal.number
2
dc.journal.pagination
546-548
dc.journal.pais
Estados Unidos
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dc.journal.ciudad
Amsterdam
dc.description.fil
Fil: Moulin, L.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Pedraza, N.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Padin, J.. Clínica “La Pequeña Familia”; Argentina
dc.description.fil
Fil: Niveyro, S.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Tuhay, G.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Rumbo, C.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Barros Schelotto, Pablo. Fundación Favaloro; Argentina
dc.description.fil
Fil: Crivelli, A.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Solar Muñiz, H.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Ramisch, D.. Fundación Favaloro; Argentina
dc.description.fil
Fil: Gondolesi, Gabriel Eduardo. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Fundación Favaloro; Argentina
dc.journal.title
Transplantation Proceedings
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dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/doi/https://dx.doi.org/10.1016/j.transproceed.2016.01.014
dc.relation.alternativeid
info:eu-repo/semantics/altIdentifier/url/https://www.sciencedirect.com/science/article/pii/S0041134516001585
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